An unique clinical presentation of choledochal cyst in middle aged female

Abstract

Choledochal cyst are congenital malformations characterized by bile duct dilatation with Intra and/or extrahepatic localization. About 80%of cases are diagnosed in childhood, so their presentation in adults is rare and repeatedly associated with complications. we report a case of 41 year old female with atypical presentation of choledochal cyst of type 1b diagnosed after Ultrasonography, CT scan and MRCP imaging & managed successfully by open radical choledochal cyst excision with hepaticojejunostomy and jejunojejunostomy. Delay in the diagnosis increases the frequency of associated biliary pathology, malignant alternation and suboptimal surgical therapy.