Pulmonary lymphangiectasia: A case report

Abstract

Congenital pulmonary lymphangiectasis [CPL] is a rare, poorly documented disease, characterized by abnormal dilatation of pulmonary lymphatics without lymphatic proliferation. This disease is seen almost exclusively in infancy and early childhood. It can usually be divided into primary [congenital] and secondary forms. The primary form presents in neonates, and the patients mostly die due to the respiratory distress, shortly after birth. Here we present a case of pulmonary lymphangiectasia in an one month old child as incidental finding on autopsy.