Ruptured sex cord stromal tumor: A rare case report

Abstract

Background: Sex cord tumor with annular tubules is a rare ovarian neoplasm that accounts for <6% sex cord stromal tumors [1]. It is seen mostly in reproductive period and less commonly in pediatric population [2]. One-third of cases are associated with hyperestrogenism and Peutz- Jegher’s syndrome. Case report: A 26 years old unmarried girl came in gynaecology OPD with pain abdomen and abdominal lump since 4 months. After necessary investigations, she was planned for elective surgery but was lost to follow-up then. After 2 months, she presented in emergency with acute pain abdomen with shock. On examination, abdominopelvic mass was felt palpable corresponding to 20 weeks. Exploratory laparotomy with left sided salpingo-oopherectomy was performed. Hemoperitoneum of around 2 litres and a left-sided ovarian tumor 15x10cm in size with necrosis, hemorrhage and ruptured capsule was found. On histopathology report it was confirmed to be as sex cord tumor with annular tubules (SCTAT).Conclusion: We describe for the first time to the best of our literature search the incidental detection of SCTAT in a patient previously thought to be case of germ cell tumor. Meticulous histological staining and awareness is required for detection of such unusual incidental lesions.