article Open AccessTop 10% cited
Malignant peripheral nerve sheath tumours in neurofibromatosis 1
Journal of Medical Genetics · 2002 · Vol. 39(5) · pp. 311–314
D. Gareth Evans✉(St Mary's Hospital)M E BaserJ McGaughran(St Mary's Hospital)S Sharif(St Mary's Hospital)E Howard(St Mary's Hospital)A Moran(The Christie Hospital)
Abstract
The lifetime risk of MPNST in NF1 is much higher than previously estimated and warrants careful surveillance and a low threshold for investigation.
Neurofibromatosis and Schwannoma CasesMeningioma and schwannoma managementBone Tumor Diagnosis and TreatmentsNeurofibromatosisMedicineMalignant peripheral nerve sheath tumorCancer registryRadiation therapyPopulationIncidence (geometry)CancerSurgeryRadiology
MeSH terms
AdolescentAdultAgedEnglandFemaleHumansLongitudinal StudiesMaleMiddle AgedNeurofibromatosis 1IncidenceSurvival RateRisk Assessment
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Guidelines for the diagnosis and management of individuals with neurofibromatosis 1
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References
A genetic study of von Recklinghausen neurofibromatosis in south east Wales. I. Prevalence, fitness, mutation rate, and effect of parental transmission on severity.
Journal of Medical Genetics · 1989 · 542 citations
Malignant peripheral nerve sheath tumors. A clinicopathologic study of 120 cases
Cancer · 1986 · 1,592 citations
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