article Open AccessTop 10% cited
A new set of criteria for the diagnosis of familial Mediterranean fever in childhood
Lara D. Veeken · 2009 · Vol. 48(4) · pp. 395–398
Fatoş Yalçınkaya✉(Ankara University)Seza Özen(Boston Children's Hospital)Zeynep Birsin Özçakar(Boston Children's Museum)Nuray Aktay(Boston Children's Museum)Nilgün Çakar(Boston Children's Museum)Ali Düzova(Boston Children's Hospital)Özgür Kasapçopur(Boston Children's Museum)Atilla Halil Elhan(Boston Children's Hospital)Beyza Doğanay Erdoğan(Boston Children's Museum)Mesı̇ha Ekı̇m(Boston Children's Museum)Nazlı Kara(Boston Children's Museum)Nermin Uncu(Boston Children's Museum)Ayşı̇n Bakkaloğlu(Boston Children's Hospital)
Abstract
It was demonstrated that although the Tel Hashomer criteria were successful in diagnosing the FMF patients in childhood, its specificity was definitely low in children. The new set of criteria has a high sensitivity and specificity for the diagnosis of FMF and is practical to use on an everyday basis.
Inflammasome and immune disordersIL-33, ST2, and ILC PathwaysAutoimmune and Inflammatory Disorders ResearchMedicineFamilial Mediterranean feverLogistic regressionInternal medicineArthritisPediatricsDisease
MeSH terms
ChildChild, PreschoolConsanguinityDiagnosis, DifferentialFemaleHealth Status IndicatorsHumansMaleFamilial Mediterranean FeverRisk FactorsSensitivity and SpecificityLogistic ModelsCase-Control StudiesAge of Onset
Citations
516
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5.51
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27
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97%
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References
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